Indifferentiated pleomorphic sarcoma of high degree of left atrial a rare entity: report of a case
Keywords:
Sarcoma, NeoplasmsAbstract
Introduction: The prevalence of primary cardiac tumors at autopsy ranges from 0.001% to 0.3%. In all age
groups, benign primary neoplasms are more common than malignant masses. Primary malignant cardiac tumors
are predominantly sarcomas in nature, can present with a variety of symptoms. The clinical presentation
depends mainly on the size of the tumor. The diagnosis of cardiac tumors is largely based on the use of multiple
imaging techniques, including cardiac computed tomography (CT), cardiovascular magnetic resonance
(CMR), and echocardiography. Histopathological study continues to be the most accurate way to detect cells
of origin. Complete surgical resection remains the goal of therapy. Neoadjuvant chemotherapy should be
started once a definitive diagnosis is made, cardiac sarcoma is a lethal tumor with a median survival of 25
months.
Objective: To describe a clinical case of high-grade undifferentiated pleomorphic sarcoma of the left atrium,
an infrequent entity.
Material and methods: Retrospective descriptive study, presentation of a high-grade undifferentiated pleomorphic
sarcoma of the left atrium, an infrequent entity.
Results: The case of a 66-year-old patient who was admitted due to presenting symptoms compatible with
atypical pneumonia is presented. In this case, when no improvement was found, complementary requests were
made, concluding high-grade undifferentiated pleomorphic sarcoma, mass exceresis was performed, without
However, the patient dies approximately 3 months after cardiopulmonary complications.
Conclusions: The low frequency of presentation of primary heart sarcomas, as well as the diagnostic challenge
they imply, makes it important to know their current situation and management.
Downloads
Published
Issue
Section
License
Authors who publish with this journal agree to the following terms:
- Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution License 4.0 that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal.
- Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
- Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work.
