Herlyn-Wener-Wunderlich syndrome.

Abstract

Introduction: Herlyn-Wener-Wunderlich Syndrome is a malformation of the ducts of Muller and Wolf, due to a lack of fusion of them, is very rare and is characterized by a didelfo uterus, with a blocked hemivagina and ipsilateral renal agenesis, more common right-hand.

Objective: Describe a clinical case of a teenage patient with secondary dysmenorrhea to Herlyn-Wener-Wunderlich Syndrome.

Material and methods: A descriptive, retrospective and documentary study was conducted on secondary dysmenorrhea, mullerian malformations and presentation of a clinical case.

Results: It describes the case of a 13-year-old patient treated in the Infant Maternal Unit of the Hospital Theodoro Maldonado Carbo, with severe dysmenorrhea from the beginning of the menarch, has painful pelvic mass to palpation, abdominal ultrasound and pelvic ultrasound is performed finding two tumoration of liquid content with sediment that extend to the vaginal canal and compromising bilobed cervix, the abdominal ultrasound reports absence of right kidney so she was subjected to exploratory laparotomy confirming the diagnosis of uterine malformation with didelfo uterus, blind right hemivagina and hematocolpos.

Conclusions: Mullerian malformations correspond to rare congenital abnormalities and Herlyn-Wener-Wunderlich Syndrome is a much less common entity, causing severe dysmenorrhea, acute abdomen, clinical diagnosis is difficult and requires clinical studies Complementary. Treatment is conservative in order to preserve the patient's reproductive function